Title Information
Title
The Molecular Basis of Calcineurin Inhibition by Protein Regulators
Name: Personal
Name Part
Grigoriu, Simina r
Role
Role Term: Text
creator
Origin Information
Copyright Date
2013
Physical Description
Extent
xxxii, 287 p.
digitalOrigin
born digital
Note
Thesis (Ph.D. -- Brown University (2013)
Name: Personal
Name Part
Peti, Wolfgang
Role
Role Term: Text
Director
Name: Personal
Name Part
Delaney, Sarah
Role
Role Term: Text
Reader
Name: Personal
Name Part
Fairbrother, William
Role
Role Term: Text
Reader
Name: Personal
Name Part
Jogl, Gerwald
Role
Role Term: Text
Reader
Name: Personal
Name Part
Ellman, Jonathan
Role
Role Term: Text
Reader
Name: Corporate
Name Part
Brown University. BIOMED: Molecular Biology, Cell Biology, and Biochemistry
Role
Role Term: Text
sponsor
Genre (aat)
theses
Subject
Topic
calcineurin
Subject
Topic
PP3
Subject
Topic
PP2B
Subject
Topic
A238L
Subject
Topic
RCAN1
Subject
Topic
FK506
Subject
Topic
Cyclosporin A
Subject
Topic
immunosuppressant
Subject
Topic
immunophillin
Subject
Topic
FKBP
Subject
Topic
cyclophilin
Subject
Topic
LxVP
Subject
Topic
PxIxIT
Subject
Topic
ITC
Subject
Topic
NMR
Subject
Topic
NFAT
Subject
Topic
RII
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/886005")
Topic
Cyclosporine
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/968037")
Topic
Immunosuppressive agents
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/1057585")
Topic
Peptidylprolyl isomerase
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/1061322")
Topic
Phosphatases
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/1181820")
Topic
X-ray crystallography
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/844035")
Topic
Calcium
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/1061482")
Topic
Phosphorylation
Subject (FAST) (authorityURI="http://id.worldcat.org/fast", valueURI="http://id.worldcat.org/fast/1024778")
Topic
Molecular dynamics
Record Information
Record Content Source (marcorg)
RPB
Record Creation Date (encoding="iso8601")
20131219
Language
Language Term: Code (ISO639-2B)
eng
Language Term: Text
English
Abstract
Ser/Thr phosphatases dephosphorylate their targets with high specificity, yet the structural determinants of substrate recognition and dephosphorylation are poorly understood. Calcineurin (CN) is a conserved Ca2+/calmodulin-dependent Ser/Thr phosphatase that regulates many cellular functions and is the direct target of the immunosuppressant drugs FK506 and cyclosporin A (CSA). CN dephosphorylates the NFAT family of transcription factors, which then activate transcription of genes required for various cellular functions. This dissertation describes the structural basis for CN-substrate recognition and provides insight into the molecular mechanisms used by CN inhibitors. <br/> <br/> To investigate CN-substrate recognition we used X-ray crystallography, biochemistry, molecular dynamics simulations and in vivo experiments to study A238L, a viral protein inhibitor of CN and a substrate mimic. The 1.7 Å structure of the A238L-CN complex provides the first structural description of how CN recognizes substrates via the conserved "LxVP" motif, and enabled molecular dynamics simulations that provided the first description of substrate dephosphorylation by a Ser/Thr phosphatase. The structure also revealed that A238L competitively inhibits CN by occupying the PxIxIT and LxVP substrate recognition sites to prevent substrate docking, leaving the catalytic center fully accessible. This study establishes that FK506 and CSA also bind to the CN LxVP site to prevent LxVP-mediated substrate recognition. This highlights the importance of this interaction for substrate dephosphorylation and provides a structural basis for the development of new CN inhibitors. <br/> <br/> To gain further insight into CN regulation, we used NMR spectroscopy and isothermal titration calorimetry to characterize CN inhibition by the endogenous regulator RCAN1. NMR studies of free RCAN1 showed that it belongs to a family of proteins known as intrinsically disordered proteins, which are characterized by their lack of tertiary structure. However, we identified two partially populated α-helices in RCAN1, which are likely important for the ability of RCAN1 to act as both an inhibitor and an enhancer of CN activity. RCAN1 is overexpressed in individuals with Down syndrome, and its inhibition of CN directly correlated with symptoms of this disease. Therefore, these findings significantly advance our understanding of the underlying mechanism of Down syndrome.
Identifier: DOI
10.7301/Z0765CPQ
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In Copyright
Access Condition: restriction on access
Collection is open for research.
Type of Resource (primo)
dissertations